Novel Molecular Mechanisms Involved in the Medical Treatment of Pulmonary Arterial Hypertension

Pulmonary arterial hypertension (PAH) is a severe condition with a high mortality rate despite advances in diagnostic and therapeutic strategies. In recent years, significant scientific progress has been made in the understanding of the underlying pathobiological mechanisms. Since current available...

Descripción completa

Detalles Bibliográficos
Autores: Martín de Miguel, Irene, Cruz Utrilla, Alejandro, Oliver, Eduardo, Escribano-Subias, Pilar
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2023
País:España
Institución:Consejo Superior de Investigaciones Científicas (CSIC)
Repositorio:DIGITAL.CSIC. Repositorio Institucional del CSIC
OAI Identifier:oai:digital.csic.es:10261/296666
Acceso en línea:http://hdl.handle.net/10261/296666
Access Level:acceso abierto
Palabra clave:Pulmonary arterial hypertension
Vascular remodeling
Endothelial dysfunction
BMP signaling
Tyrosine kinase receptor
Inflammation
Epigenetics
Mitochondrial dysfunction
Descripción
Sumario:Pulmonary arterial hypertension (PAH) is a severe condition with a high mortality rate despite advances in diagnostic and therapeutic strategies. In recent years, significant scientific progress has been made in the understanding of the underlying pathobiological mechanisms. Since current available treatments mainly target pulmonary vasodilation, but lack an effect on the pathological changes that develop in the pulmonary vasculature, there is need to develop novel therapeutic compounds aimed at antagonizing the pulmonary vascular remodeling. This review presents the main molecular mechanisms involved in the pathobiology of PAH, discusses the new molecular compounds currently being developed for the medical treatment of PAH and assesses their potential future role in the therapeutic algorithms of PAH.