Inborn errors of immunity causing pediatric susceptibility to fungal diseases

Inborn errors of immunity are a heterogeneous group of genetically determined disorders that compromise the immune system, predisposing patients to infections, autoinflammatory/autoimmunity syndromes, atopy/allergies, lymphoproliferative disorders, and/or malignancies. An emerging manifestation is s...

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Detalles Bibliográficos
Autores: Olbrich, Peter, Vinh, Donald C.
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2023
País:España
Institución:Universidad de Sevilla (US)
Repositorio:idUS. Depósito de Investigación de la Universidad de Sevilla
OAI Identifier:oai:idus.us.es:11441/149150
Acceso en línea:https://hdl.handle.net/11441/149150
https://doi.org/10.3390/jof9020149
Access Level:acceso abierto
Palabra clave:Inborn errors of immunity
Primary immunodeficiency
Fungi
Mycoses
Invasive fungal disease
Superficial fungal disease
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spelling Inborn errors of immunity causing pediatric susceptibility to fungal diseasesOlbrich, PeterVinh, Donald C.Inborn errors of immunityPrimary immunodeficiencyFungiMycosesInvasive fungal diseaseSuperficial fungal diseaseInborn errors of immunity are a heterogeneous group of genetically determined disorders that compromise the immune system, predisposing patients to infections, autoinflammatory/autoimmunity syndromes, atopy/allergies, lymphoproliferative disorders, and/or malignancies. An emerging manifestation is susceptibility to fungal disease, caused by yeasts or moulds, in a superficial or invasive fashion. In this review, we describe recent advances in the field of inborn errors of immunity associated with increased susceptibility to fungal disease.MDPIFarmacología, Pediatría y RadiologíaAgencia de Innovación y Desarrollo de AndalucíaInstituto de Salud Carlos III, Madrid2023info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfapplication/pdfhttps://hdl.handle.net/11441/149150https://doi.org/10.3390/jof9020149reponame:idUS. Depósito de Investigación de la Universidad de Sevillainstname:Universidad de Sevilla (US)InglésJOURNAL OF FUNGI, 9 (2).PI-0184-2018PI19/01471https://www.mdpi.com/2309-608X/9/2/149info:eu-repo/semantics/openAccessoai:idus.us.es:11441/1491502026-06-17T12:51:07Z
dc.title.none.fl_str_mv Inborn errors of immunity causing pediatric susceptibility to fungal diseases
title Inborn errors of immunity causing pediatric susceptibility to fungal diseases
spellingShingle Inborn errors of immunity causing pediatric susceptibility to fungal diseases
Olbrich, Peter
Inborn errors of immunity
Primary immunodeficiency
Fungi
Mycoses
Invasive fungal disease
Superficial fungal disease
title_short Inborn errors of immunity causing pediatric susceptibility to fungal diseases
title_full Inborn errors of immunity causing pediatric susceptibility to fungal diseases
title_fullStr Inborn errors of immunity causing pediatric susceptibility to fungal diseases
title_full_unstemmed Inborn errors of immunity causing pediatric susceptibility to fungal diseases
title_sort Inborn errors of immunity causing pediatric susceptibility to fungal diseases
dc.creator.none.fl_str_mv Olbrich, Peter
Vinh, Donald C.
author Olbrich, Peter
author_facet Olbrich, Peter
Vinh, Donald C.
author_role author
author2 Vinh, Donald C.
author2_role author
dc.contributor.none.fl_str_mv Farmacología, Pediatría y Radiología
Agencia de Innovación y Desarrollo de Andalucía
Instituto de Salud Carlos III, Madrid
dc.subject.none.fl_str_mv Inborn errors of immunity
Primary immunodeficiency
Fungi
Mycoses
Invasive fungal disease
Superficial fungal disease
topic Inborn errors of immunity
Primary immunodeficiency
Fungi
Mycoses
Invasive fungal disease
Superficial fungal disease
description Inborn errors of immunity are a heterogeneous group of genetically determined disorders that compromise the immune system, predisposing patients to infections, autoinflammatory/autoimmunity syndromes, atopy/allergies, lymphoproliferative disorders, and/or malignancies. An emerging manifestation is susceptibility to fungal disease, caused by yeasts or moulds, in a superficial or invasive fashion. In this review, we describe recent advances in the field of inborn errors of immunity associated with increased susceptibility to fungal disease.
publishDate 2023
dc.date.none.fl_str_mv 2023
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://hdl.handle.net/11441/149150
https://doi.org/10.3390/jof9020149
url https://hdl.handle.net/11441/149150
https://doi.org/10.3390/jof9020149
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv JOURNAL OF FUNGI, 9 (2).
PI-0184-2018
PI19/01471
https://www.mdpi.com/2309-608X/9/2/149
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv MDPI
publisher.none.fl_str_mv MDPI
dc.source.none.fl_str_mv reponame:idUS. Depósito de Investigación de la Universidad de Sevilla
instname:Universidad de Sevilla (US)
instname_str Universidad de Sevilla (US)
reponame_str idUS. Depósito de Investigación de la Universidad de Sevilla
collection idUS. Depósito de Investigación de la Universidad de Sevilla
repository.name.fl_str_mv
repository.mail.fl_str_mv
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