Inborn errors of immunity causing pediatric susceptibility to fungal diseases
Inborn errors of immunity are a heterogeneous group of genetically determined disorders that compromise the immune system, predisposing patients to infections, autoinflammatory/autoimmunity syndromes, atopy/allergies, lymphoproliferative disorders, and/or malignancies. An emerging manifestation is s...
| Autores: | , |
|---|---|
| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2023 |
| País: | España |
| Institución: | Universidad de Sevilla (US) |
| Repositorio: | idUS. Depósito de Investigación de la Universidad de Sevilla |
| OAI Identifier: | oai:idus.us.es:11441/149150 |
| Acceso en línea: | https://hdl.handle.net/11441/149150 https://doi.org/10.3390/jof9020149 |
| Access Level: | acceso abierto |
| Palabra clave: | Inborn errors of immunity Primary immunodeficiency Fungi Mycoses Invasive fungal disease Superficial fungal disease |
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Inborn errors of immunity causing pediatric susceptibility to fungal diseasesOlbrich, PeterVinh, Donald C.Inborn errors of immunityPrimary immunodeficiencyFungiMycosesInvasive fungal diseaseSuperficial fungal diseaseInborn errors of immunity are a heterogeneous group of genetically determined disorders that compromise the immune system, predisposing patients to infections, autoinflammatory/autoimmunity syndromes, atopy/allergies, lymphoproliferative disorders, and/or malignancies. An emerging manifestation is susceptibility to fungal disease, caused by yeasts or moulds, in a superficial or invasive fashion. In this review, we describe recent advances in the field of inborn errors of immunity associated with increased susceptibility to fungal disease.MDPIFarmacología, Pediatría y RadiologíaAgencia de Innovación y Desarrollo de AndalucíaInstituto de Salud Carlos III, Madrid2023info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfapplication/pdfhttps://hdl.handle.net/11441/149150https://doi.org/10.3390/jof9020149reponame:idUS. Depósito de Investigación de la Universidad de Sevillainstname:Universidad de Sevilla (US)InglésJOURNAL OF FUNGI, 9 (2).PI-0184-2018PI19/01471https://www.mdpi.com/2309-608X/9/2/149info:eu-repo/semantics/openAccessoai:idus.us.es:11441/1491502026-06-17T12:51:07Z |
| dc.title.none.fl_str_mv |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| title |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| spellingShingle |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases Olbrich, Peter Inborn errors of immunity Primary immunodeficiency Fungi Mycoses Invasive fungal disease Superficial fungal disease |
| title_short |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| title_full |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| title_fullStr |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| title_full_unstemmed |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| title_sort |
Inborn errors of immunity causing pediatric susceptibility to fungal diseases |
| dc.creator.none.fl_str_mv |
Olbrich, Peter Vinh, Donald C. |
| author |
Olbrich, Peter |
| author_facet |
Olbrich, Peter Vinh, Donald C. |
| author_role |
author |
| author2 |
Vinh, Donald C. |
| author2_role |
author |
| dc.contributor.none.fl_str_mv |
Farmacología, Pediatría y Radiología Agencia de Innovación y Desarrollo de Andalucía Instituto de Salud Carlos III, Madrid |
| dc.subject.none.fl_str_mv |
Inborn errors of immunity Primary immunodeficiency Fungi Mycoses Invasive fungal disease Superficial fungal disease |
| topic |
Inborn errors of immunity Primary immunodeficiency Fungi Mycoses Invasive fungal disease Superficial fungal disease |
| description |
Inborn errors of immunity are a heterogeneous group of genetically determined disorders that compromise the immune system, predisposing patients to infections, autoinflammatory/autoimmunity syndromes, atopy/allergies, lymphoproliferative disorders, and/or malignancies. An emerging manifestation is susceptibility to fungal disease, caused by yeasts or moulds, in a superficial or invasive fashion. In this review, we describe recent advances in the field of inborn errors of immunity associated with increased susceptibility to fungal disease. |
| publishDate |
2023 |
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2023 |
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info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
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article |
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publishedVersion |
| dc.identifier.none.fl_str_mv |
https://hdl.handle.net/11441/149150 https://doi.org/10.3390/jof9020149 |
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https://hdl.handle.net/11441/149150 https://doi.org/10.3390/jof9020149 |
| dc.language.none.fl_str_mv |
Inglés |
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Inglés |
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JOURNAL OF FUNGI, 9 (2). PI-0184-2018 PI19/01471 https://www.mdpi.com/2309-608X/9/2/149 |
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info:eu-repo/semantics/openAccess |
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openAccess |
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application/pdf application/pdf |
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MDPI |
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MDPI |
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Universidad de Sevilla (US) |
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idUS. Depósito de Investigación de la Universidad de Sevilla |
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