id ES_0ce2cb9de1ce32606a71ea6e0fa8e017
oai_identifier_str oai:digital.csic.es:10261/372621
network_acronym_str ES
network_name_str España
repository_id_str
dc.title.none.fl_str_mv Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
title Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
spellingShingle Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
Borrego Yaniz, Gonzalo
title_short Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
title_full Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
title_fullStr Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
title_full_unstemmed Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
title_sort Risk loci involved in giant cell arteritis susceptibility: a genome-wide association study
dc.creator.none.fl_str_mv Borrego Yaniz, Gonzalo
Ortiz-Fernández, Lourdes
Madrid-Paredes, Adela
Kerick, Martin
Hernández-Rodríguez, José
Mackie, Sarah
Vaglio, Augusto
Castañeda, Santos
Solans, Roser
Khalidi, Nader
Langford, Carol
Ytterberg, Steven R.
Beretta, Lorenzo
Govoni, Marcelo
Emmi, Giacomo
Cimmino, Marco A.
Witte, Torsten
Neumann, Thomas
Holle, Julia
Schönau, Verena
Pugnet, Gregory
Papo, Thomas
Haroche, Julien
Mahr, Alfred
Mouthon, Luc
Molberg, Oyvind
Diamantopoulos, Andreas P.
Voskuyl, Alexandre E.
Daikeler, Thomas
Berger, Christoph
Molloy, Eamonn
Blockmans, Daniel
Ortego-Centeno, Norberto
Brouwer, Elisabeth
Lamprecht, Peter
Klapa, Sebastian
Salvarani, Carlo
Merkel, Peter A.
Cid, María C.
González-Gay, Miguel A.
Morgan, Ann W.
Martín, Javier
Márquez, Ana
Spanish GCA Study Group
UK GCA Consortium
Vasculitis Clinical Research Consortium
author Borrego Yaniz, Gonzalo
author_facet Borrego Yaniz, Gonzalo
Ortiz-Fernández, Lourdes
Madrid-Paredes, Adela
Kerick, Martin
Hernández-Rodríguez, José
Mackie, Sarah
Vaglio, Augusto
Castañeda, Santos
Solans, Roser
Khalidi, Nader
Langford, Carol
Ytterberg, Steven R.
Beretta, Lorenzo
Govoni, Marcelo
Emmi, Giacomo
Cimmino, Marco A.
Witte, Torsten
Neumann, Thomas
Holle, Julia
Schönau, Verena
Pugnet, Gregory
Papo, Thomas
Haroche, Julien
Mahr, Alfred
Mouthon, Luc
Molberg, Oyvind
Diamantopoulos, Andreas P.
Voskuyl, Alexandre E.
Daikeler, Thomas
Berger, Christoph
Molloy, Eamonn
Blockmans, Daniel
Ortego-Centeno, Norberto
Brouwer, Elisabeth
Lamprecht, Peter
Klapa, Sebastian
Salvarani, Carlo
Merkel, Peter A.
Cid, María C.
González-Gay, Miguel A.
Morgan, Ann W.
Martín, Javier
Márquez, Ana
Spanish GCA Study Group
UK GCA Consortium
Vasculitis Clinical Research Consortium
author_role author
author2 Ortiz-Fernández, Lourdes
Madrid-Paredes, Adela
Kerick, Martin
Hernández-Rodríguez, José
Mackie, Sarah
Vaglio, Augusto
Castañeda, Santos
Solans, Roser
Khalidi, Nader
Langford, Carol
Ytterberg, Steven R.
Beretta, Lorenzo
Govoni, Marcelo
Emmi, Giacomo
Cimmino, Marco A.
Witte, Torsten
Neumann, Thomas
Holle, Julia
Schönau, Verena
Pugnet, Gregory
Papo, Thomas
Haroche, Julien
Mahr, Alfred
Mouthon, Luc
Molberg, Oyvind
Diamantopoulos, Andreas P.
Voskuyl, Alexandre E.
Daikeler, Thomas
Berger, Christoph
Molloy, Eamonn
Blockmans, Daniel
Ortego-Centeno, Norberto
Brouwer, Elisabeth
Lamprecht, Peter
Klapa, Sebastian
Salvarani, Carlo
Merkel, Peter A.
Cid, María C.
González-Gay, Miguel A.
Morgan, Ann W.
Martín, Javier
Márquez, Ana
Spanish GCA Study Group
UK GCA Consortium
Vasculitis Clinical Research Consortium
author2_role author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
dc.contributor.none.fl_str_mv Instituto de Salud Carlos III
Ministerio de Ciencia e Innovación (España)
National Institute for Health and Care Research (US)
Medical Research Council (UK)
European Commission
Consejo Superior de Investigaciones Científicas [https://ror.org/02gfc7t72]
description et al.
publishDate 2024
dc.date.none.fl_str_mv 2024
2024
2024
dc.type.none.fl_str_mv info:eu-repo/semantics/article
http://purl.org/coar/resource_type/c_6501
Publisher's version
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv http://hdl.handle.net/10261/372621
url http://hdl.handle.net/10261/372621
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv #PLACEHOLDER_PARENT_METADATA_VALUE#
#PLACEHOLDER_PARENT_METADATA_VALUE#
#PLACEHOLDER_PARENT_METADATA_VALUE#
info:eu-repo/grantAgreement/EC/H2020/831514
info:eu-repo/grantAgreement/AEI/Plan Estatal de Investigación Científica y Técnica y de Innovación 2017-2020/PID2020-114909RB-I00
info:eu-repo/grantAgreement/AEI//IJC2019-040746-I
The underlying dataset has been published as supplementary material of the article in the publisher platform at DOI 10.1016/S2665-9913(24)00064-X
https://doi.org/10.1016/ S2665-9913(24)00064-X

dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Elsevier
publisher.none.fl_str_mv Elsevier
dc.source.none.fl_str_mv reponame:DIGITAL.CSIC. Repositorio Institucional del CSIC
instname:Consejo Superior de Investigaciones Científicas (CSIC)
instname_str Consejo Superior de Investigaciones Científicas (CSIC)
reponame_str DIGITAL.CSIC. Repositorio Institucional del CSIC
collection DIGITAL.CSIC. Repositorio Institucional del CSIC
repository.name.fl_str_mv
repository.mail.fl_str_mv
_version_ 1869403309057507328
spelling Risk loci involved in giant cell arteritis susceptibility: a genome-wide association studyBorrego Yaniz, GonzaloOrtiz-Fernández, LourdesMadrid-Paredes, AdelaKerick, MartinHernández-Rodríguez, JoséMackie, SarahVaglio, AugustoCastañeda, SantosSolans, RoserKhalidi, NaderLangford, CarolYtterberg, Steven R.Beretta, LorenzoGovoni, MarceloEmmi, GiacomoCimmino, Marco A.Witte, TorstenNeumann, ThomasHolle, JuliaSchönau, VerenaPugnet, GregoryPapo, ThomasHaroche, JulienMahr, AlfredMouthon, LucMolberg, OyvindDiamantopoulos, Andreas P.Voskuyl, Alexandre E.Daikeler, ThomasBerger, ChristophMolloy, EamonnBlockmans, DanielOrtego-Centeno, NorbertoBrouwer, ElisabethLamprecht, PeterKlapa, SebastianSalvarani, CarloMerkel, Peter A.Cid, María C.González-Gay, Miguel A.Morgan, Ann W.Martín, JavierMárquez, AnaSpanish GCA Study GroupUK GCA ConsortiumVasculitis Clinical Research Consortiumet al.[Background] Giant cell arteritis is an age-related vasculitis that mainly affects the aorta and its branches in individuals aged 50 years and older. Current options for diagnosis and treatment are scarce, highlighting the need to better understand its underlying pathogenesis. Genome-wide association studies (GWAS) have emerged as a powerful tool for unravelling the pathogenic mechanisms involved in complex diseases. We aimed to characterise the genetic basis of giant cell arteritis by performing the largest GWAS of this vasculitis to date and to assess the functional consequences and clinical implications of identified risk loci.[Methods] We collected and meta-analysed genomic data from patients with giant cell arteritis and healthy controls of European ancestry from ten cohorts across Europe and North America. Eligible patients required confirmation of giant cell arteritis diagnosis by positive temporal artery biopsy, positive temporal artery doppler ultrasonography, or imaging techniques confirming large-vessel vasculitis. We assessed the functional consequences of loci associated with giant cell arteritis using cell enrichment analysis, fine-mapping, and causal gene prioritisation. We also performed a drug repurposing analysis and developed a polygenic risk score to explore the clinical implications of our findings.[Findings] We included a total of 3498 patients with giant cell arteritis and 15 550 controls. We identified three novel loci associated with risk of giant cell arteritis. Two loci, MFGE8 (rs8029053; p=4·96 × 10–8; OR 1·19 [95% CI 1·12–1·26]) and VTN (rs704; p=2·75 × 10–9; OR 0·84 [0·79–0·89]), were related to angiogenesis pathways and the third locus, CCDC25 (rs11782624; p=1·28 × 10–8; OR 1·18 [1·12–1·25]), was related to neutrophil extracellular traps (NETs). We also found an association between this vasculitis and HLA region and PLG. Variants associated with giant cell arteritis seemed to fulfil a specific regulatory role in crucial immune cell types. Furthermore, we identified several drugs that could represent promising candidates for treatment of this disease. The polygenic risk score model was able to identify individuals at increased risk of developing giant cell arteritis (90th percentile OR 2·87 [95% CI 2·15–3·82]; p=1·73 × 10–13).[Interpretation] We have found several additional loci associated with giant cell arteritis, highlighting the crucial role of angiogenesis in disease susceptibility. Our study represents a step forward in the translation of genomic findings to clinical practice in giant cell arteritis, proposing new treatments and a method to measure genetic predisposition to this vasculitis.Institute of Health Carlos III, Spanish Ministry of Science and Innovation, UK Medical Research Council, and National Institute for Health and Care ResearchMCC reports support from the Spanish Ministry of Science and Innovation (PID2020-114909RB-I00), EU/EFPIA/Innovative Medicines Initiative 2 Joint Undertaking Immune-Image grant no 831514. LO-F was supported by a Juan de la Cierva Incorporación fellowship (IJC2019-040746-I), funded by MCIN/AEI/10.13039/501100011033.Peer reviewedElsevierInstituto de Salud Carlos IIIMinisterio de Ciencia e Innovación (España)National Institute for Health and Care Research (US)Medical Research Council (UK)European CommissionConsejo Superior de Investigaciones Científicas [https://ror.org/02gfc7t72]202420242024info:eu-repo/semantics/articlehttp://purl.org/coar/resource_type/c_6501Publisher's versioninfo:eu-repo/semantics/publishedVersionapplication/pdfhttp://hdl.handle.net/10261/372621reponame:DIGITAL.CSIC. Repositorio Institucional del CSICinstname:Consejo Superior de Investigaciones Científicas (CSIC)Inglés#PLACEHOLDER_PARENT_METADATA_VALUE##PLACEHOLDER_PARENT_METADATA_VALUE##PLACEHOLDER_PARENT_METADATA_VALUE#info:eu-repo/grantAgreement/EC/H2020/831514info:eu-repo/grantAgreement/AEI/Plan Estatal de Investigación Científica y Técnica y de Innovación 2017-2020/PID2020-114909RB-I00info:eu-repo/grantAgreement/AEI//IJC2019-040746-IThe underlying dataset has been published as supplementary material of the article in the publisher platform at DOI 10.1016/S2665-9913(24)00064-Xhttps://doi.org/10.1016/ S2665-9913(24)00064-XSíinfo:eu-repo/semantics/openAccessoai:digital.csic.es:10261/3726212026-05-22T06:33:51Z
score 15,811543