New microdeletion and microduplication syndromes : a comprehensive review

Several new microdeletion and microduplication syndromes are emerging as disorders that have been proven to cause multisystem pathologies frequently associated with intellectual disability (ID), multiple congenital anomalies (MCA), autistic spectrum disorders (ASD) and other phenotypic findings. In...

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Detalles Bibliográficos
Autores: Nevado Blanco, Julián, Mergener, Rafaella, Palomares-Bralo, María, Souza, Karen Regina Silva de, Vallespín García, Elena, Mena, Rocío, Martínez-Glez, Víctor, Palomino, María Ángeles, Santos Simarro, Fernando, García Miñaur, Sixto, García Santiago, Fé Amalia, Mansilla Aparicio, Elena, Fernández García-Moya, Luis, Torres Pérez Hidalgo, María Luisa de, Mariluce Riegel, Mariluce Riegel, Lapunzina Badía, Pablo D.
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2014
País:Brasil
Institución:Universidade Federal do Rio Grande do Sul (UFRGS)
Repositorio:Repositório Institucional da UFRGS
Idioma:inglés
OAI Identifier:oai:www.lume.ufrgs.br:10183/116917
Acceso en línea:http://hdl.handle.net/10183/116917
Access Level:acceso abierto
Palabra clave:Duplicação cromossômica
Deleção cromossômica
Rearranjo gênico
Microdeletion
Microduplication
Chromosome rearrangement
Novel deletions
Novel duplications
Descripción
Sumario:Several new microdeletion and microduplication syndromes are emerging as disorders that have been proven to cause multisystem pathologies frequently associated with intellectual disability (ID), multiple congenital anomalies (MCA), autistic spectrum disorders (ASD) and other phenotypic findings. In this paper, we review the “new” and emergent microdeletion and microduplication syndromes that have been described and recognized in recent years with the aim of summarizing their main characteristics and chromosomal regions involved. We decided to group them by genomic region and within these groupings have classified them into those that include ID, MCA, ASD or other findings. This review does not intend to be exhaustive but is rather a quick guide to help pediatricians, clinical geneticists, cytogeneticists and/or molecular geneticists.