Síndrome do nevus organóide: relato de caso
The authors present a case of a child with organoid nevus syndrome, characterized by epibulbar choristoma in the right eye, Jadassohn's nevus sebaceous in the scalp and arachnoid cist. The pathology of the ocular lesion revealed a mixture of ectodermal and mesodermal elements, leding to the rar...
| Autores: | , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2001 |
| País: | Brasil |
| Institución: | Universidade Federal de São Paulo (UNIFESP) |
| Repositorio: | Repositório Institucional da UNIFESP |
| Idioma: | portugués |
| OAI Identifier: | oai:repositorio.unifesp.br:11600/1206 |
| Acceso en línea: | http://dx.doi.org/10.1590/S0004-27492001000400016 http://repositorio.unifesp.br/handle/11600/1206 |
| Access Level: | acceso abierto |
| Palabra clave: | Nevus Hamartoma Choristoma Neurocutaneous syndromes Eye neoplasms Organoids Case report Child Nevo Coristoma Sindromes neurocutâneas Neoplasias oculares Organóides Relato de caso Criança |
| Sumario: | The authors present a case of a child with organoid nevus syndrome, characterized by epibulbar choristoma in the right eye, Jadassohn's nevus sebaceous in the scalp and arachnoid cist. The pathology of the ocular lesion revealed a mixture of ectodermal and mesodermal elements, leding to the rare diagnosis of epibulbar complex choristoma.The syndrome is rarely described in the ophthalmologic literature. Some considerations are made regarding ophthalmologic and systemic associations. |
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