p53 gene analysis in childhood B non - Hodgkin’s lymphoma

CONTEXT: Mutations or deletions in the tumor- suppressor gene p53 are among the commonest genetic changes found in human neoplasms including breast, lung and bowel cancers. In hematological malignancies, p53 is most often mutated in Burkitt’s lymphoma, with p53 mutations present in 30 to 40% of tumo...

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Detalles Bibliográficos
Autores: Klumb, Claudete Esteves Nogueira Pinto, Resende, Lídia Maria Magalhães de, Tajara, Eloísa Helena, Bertelli, Erika Cristina Pavarino, Rumjanek, Vivian Mary, Maia, Raquel Ciuvalschi
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2001
País:Brasil
Institución:Associação Paulista de Medicina
Repositorio:São Paulo medical journal (Online)
Idioma:inglés
OAI Identifier:oai:ojs.diagnosticoetratamento.emnuvens.com.br:article/2787
Acceso en línea:https://periodicosapm.emnuvens.com.br/spmj/article/view/2787
Access Level:acceso abierto
Palabra clave:Mutação do gene p53
Linfoma não-Hodgkin
Linfoma de Burkitt
p53 mutation
B non-Hodgkin’s lymphoma
Burkitt’s lymphoma
Descripción
Sumario:CONTEXT: Mutations or deletions in the tumor- suppressor gene p53 are among the commonest genetic changes found in human neoplasms including breast, lung and bowel cancers. In hematological malignancies, p53 is most often mutated in Burkitt’s lymphoma, with p53 mutations present in 30 to 40% of tumors amples and in 70% of cell lines. OBJECTIVE: To analyze the p53 gene alterations in child patients with B non-Hodgkin’s lymphoma. DESIGN: Descriptive study. SETTING: Tertiary oncology care center. PARTICIPANTS: The study investigated 12 patients with childhood B non-Hodgkin’s lymphoma (Burkitt’s lymphoma).Screening for p53 mutations was done by polymerase chain reaction - single strand conformation alpolymorphism (PCR-SSCP) analysis of exon 5 to 8/9 of the gene. RESULTS: Abnormal polymerase chain reaction - single strand conformational polymorphism migration pattern was observed in 4 patients (33.3%), one on exon 6 and three on exon 7. Positive cases included 2 patients who died from disease. CONCLUSION: These preliminary results suggest that p53 mutations are quite frequent in children with Burkitt’s lymphoma and may play a role in lymphoma genesis or disease progression.