Dermatomiosite juvenil (DMJ) e comprometimento pulmonar grave: relato de caso

Juvenile dermatomyositis (JDM) is an inflammatory, non-pustular disorder of skeletal muscles and skin. Other organs, such as the lungs, can be involved. Pulmonary complications are associated with high morbimortality rates and can develop in the acute phase of the disease. Due to its rarity, diagnos...

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Detalles Bibliográficos
Autores: Silva, Érika Cristina Carneiro da [UNIFESP], Bugni, Vanessa Monteiro [UNIFESP], Terreri, Maria Teresa Ramos Ascensão [UNIFESP], Castro, Márcia Helena de Oliveira [UNIFESP], Ishigai, Márcia Marcelino de Souza [UNIFESP], Hilário, Maria Odete Esteves [UNIFESP]
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2009
País:Brasil
Institución:Universidade Federal de São Paulo (UNIFESP)
Repositorio:Repositório Institucional da UNIFESP
Idioma:portugués
OAI Identifier:oai:repositorio.unifesp.br:11600/5185
Acceso en línea:http://dx.doi.org/10.1590/S0482-50042009000400012
http://repositorio.unifesp.br/handle/11600/5185
Access Level:acceso abierto
Palabra clave:juvenile dermatomyositis
diffuse alveolar injury
dermatomiosite juvenil
dano alveolar difuso
Descripción
Sumario:Juvenile dermatomyositis (JDM) is an inflammatory, non-pustular disorder of skeletal muscles and skin. Other organs, such as the lungs, can be involved. Pulmonary complications are associated with high morbimortality rates and can develop in the acute phase of the disease. Due to its rarity, diagnosis difficulty and severity pulmonary involvement, we report the case of a 3-year-old girl with JDM and pulmonary involvement and evolution to death.