Giant Lipofibromatous Hamartoma of Median Nerve in a Child

Lipofibromatous hamartoma (LFH) is a rare fibrofatty tumor of adipocytes within peripheral nerves, affecting mainly children. It typically presents as a palpable mass surrounding the nerves of the upper limbs, causing pain and neurological deficits in the affected nerve distribution. We report the c...

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Detalles Bibliográficos
Autores: TELES FILHO, RICARDO VIEIRA, Guilherme de Matos Abe, Paulo Henrique de Aquino Júnior, Giovanni Ferreira Viggiano, Bruna Ribas Teixeira, Murilo Eugênio Oliveira
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2023
País:Brasil
Institución:Universidade Federal do Rio Grande do Sul (UFRGS)
Repositorio:Clinical and Biomedical Research
Idioma:portugués
OAI Identifier:oai:seer.ufrgs.br:article/125914
Acceso en línea:https://seer.ufrgs.br/index.php/hcpa/article/view/125914
Access Level:acceso abierto
Palabra clave:Lipofibromatous hamartoma
Median nerve
Magnetic resonance imaging
Descripción
Sumario:Lipofibromatous hamartoma (LFH) is a rare fibrofatty tumor of adipocytes within peripheral nerves, affecting mainly children. It typically presents as a palpable mass surrounding the nerves of the upper limbs, causing pain and neurological deficits in the affected nerve distribution. We report the case of a child with a 2-years presentation of a mass in the right wrist associated with pain and paresthesia, who underwent investigation with magnetic resonance imaging (MR I). It showed thickening of the median nerve with spaghetti-like appearance associated with lipomatous tissue in a coaxial cable-like pattern, both features characteristic of LFH. This case illustrates the importance of MRI in the differential diagnosis of limb masses in the pediatric population.