Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
Pulmonary alveolar proteinosis (PAP) is a rare condition of unknown etiology. It hasbeen described as the presence of periodic acid-Schiff-positive proteinaceous material(rich in lipids) in the alveoli. Its pathogenesis is believed to consist of an overproductionor surfactant removal defect at the l...
| Autores: | , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2022 |
| País: | Brasil |
| Institución: | Universidade Federal do Rio Grande do Sul (UFRGS) |
| Repositorio: | Clinical and Biomedical Research |
| Idioma: | portugués |
| OAI Identifier: | oai:seer.ufrgs.br:article/125272 |
| Acceso en línea: | https://seer.ufrgs.br/index.php/hcpa/article/view/125272 |
| Access Level: | acceso abierto |
| Palabra clave: | Proteinose alveolar paraneoplásica pulmonary alveolar proteinosis paraneoplastic |
| Sumario: | Pulmonary alveolar proteinosis (PAP) is a rare condition of unknown etiology. It hasbeen described as the presence of periodic acid-Schiff-positive proteinaceous material(rich in lipids) in the alveoli. Its pathogenesis is believed to consist of an overproductionor surfactant removal defect at the lung. The association of PAP with respiratorydiseases, silicosis, exposure to aluminium or titanium, and hematological neoplasiashas been reported. Here we report two cases of pulmonary alveolar proteinosis andneoplasm diagnosed at the PulmonaryDepartment at Hospital de Clínicas de PortoAlegre. |
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