Atypical Macular Presentation in a FRAT Case and HANAC Syndrome, A Case Report

Purpose: Report an atypical Familial Retinal Arterial Tortuosity (FRAT) case associated with Hereditary Angiopathy with Nephropathy, Aneurysm and Cramps (HANAC). Methods: The authors report the case of a female patient with FRAT and HANAC, and an asymmetric ocular presentation which is unusual in Fa...

Descripción completa

Detalles Bibliográficos
Autores: Ferreira, Felipe de Queiroz Tavares, de Queiroz, Marjorie Fornazier Do Nascimento [UNESP], da Fonseca, André Luis Ayres, de Freitas, Ana Cristina Lavor Holanda, Nascimento, Maurício Abujamra
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2021
País:Brasil
Institución:Universidade Estadual Paulista (UNESP)
Repositorio:Repositório Institucional da UNESP
Idioma:inglés
OAI Identifier:oai:repositorio.unesp.br:11449/223351
Acceso en línea:http://dx.doi.org/10.2174/1874364102115010246
http://hdl.handle.net/11449/223351
Access Level:acceso abierto
Palabra clave:Familial retinal arteriolar tortuosity
Macular hemorrhages
Retina
Retinal vascular tortuosity
Retinal vessels
Spontaneous retinal hemorrhages
Descripción
Sumario:Purpose: Report an atypical Familial Retinal Arterial Tortuosity (FRAT) case associated with Hereditary Angiopathy with Nephropathy, Aneurysm and Cramps (HANAC). Methods: The authors report the case of a female patient with FRAT and HANAC, and an asymmetric ocular presentation which is unusual in Familial Retinal Arterial Tortuosity patients. Conclusion: These findings help in better understanding this rare disease. HANAC Syndrome is not a common issue; thus, it is essential to understand it to make the right diagnosis. Careful ophthalmological examination plays a key role in this process since, in the herein reported case, it could have helped to diagnose a disease capable of affecting a patient’s health, although it was an atypical ocular impairment.