Progressive supranuclear palsy: new concepts

Progressive supranuclear palsy (PSP) is a distinctive form of neurodegenerative disease which affects the brainstem and basal ganglia. Patients present supranuclear ophthalmoplegia, postural instability and mild dementia. PSP is defined neuropathologically by the accumulation of neurofibrillary tang...

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Detalles Bibliográficos
Autores: Barsottini, Orlando Graziani Povoas [UNIFESP], Felício, André Carvalho [UNIFESP], Aquino, Camila Catherine Henriques de [UNIFESP], Pedroso, José Luiz [UNIFESP]
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2010
País:Brasil
Institución:Universidade Federal de São Paulo (UNIFESP)
Repositorio:Repositório Institucional da UNIFESP
Idioma:inglés
OAI Identifier:oai:repositorio.unifesp.br:11600/6019
Acceso en línea:http://dx.doi.org/10.1590/S0004-282X2010000600020
http://repositorio.unifesp.br/handle/11600/6019
Access Level:acceso abierto
Palabra clave:progressive supranuclear palsy
atypical parkinsonism
tauopathy
paralisia supranuclear progressiva
parkinsonismo atípico
taupatias
Descripción
Sumario:Progressive supranuclear palsy (PSP) is a distinctive form of neurodegenerative disease which affects the brainstem and basal ganglia. Patients present supranuclear ophthalmoplegia, postural instability and mild dementia. PSP is defined neuropathologically by the accumulation of neurofibrillary tangles in the subthalamic nucleus, pallidum, red nucleus, substantia nigra, striatum, pontine tegmentum, oculomotor nucleus, medulla and dentate nucleus. Over the last decade many lines of investigations have helped refine PSP in many aspects and it is the purpose of this review to help neurologists identify PSP, to better understand its pathophysiology and to provide a more focused, symptom-based treatment approach.