Linear cutaneous lupus erythematosus following the lines of Blaschko: case report

Chronic cutaneous lupus erythematosus in a linear configuration is rare, particularly in children, demonstrating similar incidence in both genders, no photo-sensitivity and lower probability of progression to systemic disease. We describe the case of a 9-year-old girl who presented erythematous papu...

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Detalles Bibliográficos
Autores: Marinho, Ayana Karla de Oliveira Ferreira, Ramos, Ticiana Batista, Barbosa, Deborah Maria de Castro, Kozmhinsky, Valter, Takano, Daniela Mayumi, Figueira, Marcella Maria de Souza Araújo
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2016
País:Brasil
Institución:Universidade Federal do Rio Grande do Norte (UFRN)
Repositorio:Repositório Institucional da UFRN
Idioma:inglés
OAI Identifier:oai:repositorio.ufrn.br:123456789/31028
Acceso en línea:https://repositorio.ufrn.br/handle/123456789/31028
Access Level:acceso abierto
Palabra clave:Lupus erythematosus - cutaneous
Lupus erythematosus -discoid
Lupus erythematosus - systemic
Mosaicism
Descripción
Sumario:Chronic cutaneous lupus erythematosus in a linear configuration is rare, particularly in children, demonstrating similar incidence in both genders, no photo-sensitivity and lower probability of progression to systemic disease. We describe the case of a 9-year-old girl who presented erythematous papules with central atrophy on the upper and lower right limbs, asymptomatic and following the lines of Blaschko, since age four. Histological examination showed atrophy of the epidermis with aggression from epidermal-dermal interface and periadnexal and perivascular lymphocytic inflammatory infiltrate. Laboratory tests showed ANAin a titer of 1:320, in a dense and fine speckled pattern. Due to the rarity of presentation and location of the disease, this case is reported here