Osteodistrofias raras do osso temporal

Temporal bone osteodysplasia can produce many different symptoms, such as involvement restricted to the temporal bone or impairment of other bones. We consider, in this study two entities that are rare osteodysplasia cases, which are osteopetrosis and Camurati-Engelmann disease, the latter being ext...

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Detalles Bibliográficos
Autores: Antunes, Marcos Luiz [UNIFESP], Testa, Jose Ricardo Gurgel [UNIFESP], Frazatto, Ricardo [UNIFESP], Barberi, Jose Antonio Ferreira [UNIFESP], Silva, Rogério Fernandes Nunes da [UNIFESP]
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2005
País:Brasil
Institución:Universidade Federal de São Paulo (UNIFESP)
Repositorio:Repositório Institucional da UNIFESP
Idioma:portugués
OAI Identifier:oai:repositorio.unifesp.br:11600/2460
Acceso en línea:https://dx.doi.org/10.1590/S0034-72992005000200018
https://repositorio.unifesp.br/handle/11600/2460
Access Level:acceso abierto
Palabra clave:Osteopetrosis
Osteodysplasia
Temporal bone
Osteopetrose
Osteodisplasias
Osso temporal
Descripción
Sumario:Temporal bone osteodysplasia can produce many different symptoms, such as involvement restricted to the temporal bone or impairment of other bones. We consider, in this study two entities that are rare osteodysplasia cases, which are osteopetrosis and Camurati-Engelmann disease, the latter being extremely rare. We present two cases of benign form of osteopetrosis (Albers-Schulenburg's disease), a patient of 11 years old and another one of 48 years old, both male, and a patient of 28 years old, female, with Camurati-Engelmann's disease. The facial palsy was a manifestation in two of the patients. We discuss some aspects about the clinical manifestations, radiological findings, as well as differential diagnostic and therapy in view of the complications of the diseases.