Turner Syndrome: Case Report

lntroduction: Turner syndromeis a chromosomopathy that affects women, it is distinguished by the partial or complete absence of the X chromosome, accompanied by a combination of characteristic phenotypic features including the presence of short stature, sexual infantiilsm, ovarian dysgenesisand majo...

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Detalles Bibliográficos
Autores: Oliveira Alves, Pollyana Cassimiro, Campos Fernandes, Regina Célia de Souza, Medina-Acosta, Enrique
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2009
País:Brasil
Institución:Faculdade de Medicina de Campos (FMC)
Repositorio:Revista Científica da Faculdade de Medicina de Campos
Idioma:portugués
OAI Identifier:oai:ojs.www.fmc.br:article/128
Acceso en línea:https://www.fmc.br/ojs/index.php/RCFMC/article/view/128
Access Level:acceso abierto
Palabra clave:Síndrome de Turner
cromossomopatia disgenesia ovariana
Turner syndrome
chromosomopathy ovarian dysgenesis
Descripción
Sumario:lntroduction: Turner syndromeis a chromosomopathy that affects women, it is distinguished by the partial or complete absence of the X chromosome, accompanied by a combination of characteristic phenotypic features including the presence of short stature, sexual infantiilsm, ovarian dysgenesisand major and minor malformations. Objective: To describe a case of Turner syndrome.Method: Review of medical record.Case report: A 2-year-old girl with recurrent ear infections history and hypertrophy of adenoid,slymphedema of extremities at birth, beyond the following physical characteristics: growth retardation, low posterior hairline, pterigium coli, short neck, micrognathia, inner canthal folds and widely spaced nipples. The diagnosis was confirmed by the quantitative fluorescent polymerase chain reaction. Thereafter the patient was evaluated for the presence of associated cardiac and renal malformations that were excluded. At thistime she was in multidisciplinary monitoring.Conclusion: This report is an opportunity for discussion of clinical manifestations, diagnostic methods, follow up, and therapeutic strategies for Turner syndrome.