Brazilian guidelines for the diagnosis and treatment of hereditary angioedema

p. 1627-1636

Detalles Bibliográficos
Autores: Bianchi, Pedro Giavina, França, Alfeu T., Grumach, Anete S., Motta, Abílio A., Fernandes, Fátima R., Campos, Régis de Albuquerque, Valle, Solange O., Rosário, Nelson A., Solé, Dirceu
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2011
País:Brasil
Institución:Universidade Federal da Bahia (UFBA)
Repositorio:Repositório Institucional da UFBA
Idioma:inglés
OAI Identifier:oai:repositorio.ufba.br:ri/18108
Acceso en línea:http://repositorio.ufba.br/ri/handle/ri/18108
Access Level:acceso abierto
Palabra clave:Hereditary angioedema
C1 inhibitor
Asphyxia
Acute surgical abdomen
Guidelines
Consensus
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network_name_str Brasil
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dc.title.pt_BR.fl_str_mv Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
dc.title.alternative.pt_BR.fl_str_mv Clinics
title Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
spellingShingle Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
Bianchi, Pedro Giavina
Hereditary angioedema
C1 inhibitor
Asphyxia
Acute surgical abdomen
Guidelines
Consensus
title_short Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
title_full Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
title_fullStr Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
title_full_unstemmed Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
title_sort Brazilian guidelines for the diagnosis and treatment of hereditary angioedema
dc.creator.none.fl_str_mv Bianchi, Pedro Giavina
França, Alfeu T.
Grumach, Anete S.
Motta, Abílio A.
Fernandes, Fátima R.
Campos, Régis de Albuquerque
Valle, Solange O.
Rosário, Nelson A.
Solé, Dirceu
Bianchi, Pedro Giavina
França, Alfeu T.
Grumach, Anete S.
Motta, Abílio A.
Fernandes, Fátima R.
Campos, Régis de Albuquerque
Valle, Solange O.
Rosário, Nelson A.
Solé, Dirceu
author Bianchi, Pedro Giavina
author_facet Bianchi, Pedro Giavina
França, Alfeu T.
Grumach, Anete S.
Motta, Abílio A.
Fernandes, Fátima R.
Campos, Régis de Albuquerque
Valle, Solange O.
Rosário, Nelson A.
Solé, Dirceu
author_role author
author2 França, Alfeu T.
Grumach, Anete S.
Motta, Abílio A.
Fernandes, Fátima R.
Campos, Régis de Albuquerque
Valle, Solange O.
Rosário, Nelson A.
Solé, Dirceu
author2_role author
author
author
author
author
author
author
author
dc.subject.por.fl_str_mv Hereditary angioedema
C1 inhibitor
Asphyxia
Acute surgical abdomen
Guidelines
Consensus
topic Hereditary angioedema
C1 inhibitor
Asphyxia
Acute surgical abdomen
Guidelines
Consensus
description p. 1627-1636
publishDate 2011
dc.date.issued.fl_str_mv 2011
dc.date.accessioned.fl_str_mv 2015-10-13T12:28:26Z
dc.date.available.fl_str_mv 2015-10-13T12:28:26Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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status_str publishedVersion
dc.identifier.uri.fl_str_mv http://repositorio.ufba.br/ri/handle/ri/18108
dc.identifier.issn.none.fl_str_mv 1807-5932,
dc.identifier.number.pt_BR.fl_str_mv v. 66, n. 9
identifier_str_mv 1807-5932,
v. 66, n. 9
url http://repositorio.ufba.br/ri/handle/ri/18108
dc.language.iso.fl_str_mv eng
language eng
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.country.fl_str_mv Brasil
dc.source.pt_BR.fl_str_mv http://dx.doi.org/10.1590/S1807-59322011000900021
dc.source.none.fl_str_mv reponame:Repositório Institucional da UFBA
instname:Universidade Federal da Bahia (UFBA)
instacron:UFBA
instname_str Universidade Federal da Bahia (UFBA)
instacron_str UFBA
institution UFBA
reponame_str Repositório Institucional da UFBA
collection Repositório Institucional da UFBA
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spelling 2015-10-13T12:28:26Z2015-10-13T12:28:26Z20111807-5932,http://repositorio.ufba.br/ri/handle/ri/18108v. 66, n. 9p. 1627-1636Hereditary angioedema is an autosomal dominant disease characterized by edema attacks with multiple organ involvement. It is caused by a quantitative or functional deficiency of the C1 inhibitor, which is a member of the serine protease inhibitor family. Hereditary angioedema is unknown to many health professionals and is therefore an underdiagnosed disease. The causes of death from hereditary angioedema include laryngeal edema with asphyxia. The estimated mortality rate in patients in whom the disease goes undetected and who are therefore incorrectly treated is 25-40%. In addition to edema of the glottis, hereditary angioedema often results in edema of the gastrointestinal tract, which can be incapacitating. Patients with hereditary angioedema may undergo unnecessary surgical interventions because the digestive tract can be the primary or only organ system involved, thus mimicking acute surgical abdomen. It is estimated that patients with hereditary angioedema experience some degree of disability 20-100 days per year. The Experts in Clinical Immunology and Allergy of the "Associação Brasileira de Alergia e Imunopatologia -ASBAI" developed these guidelines for the diagnosis, therapy, and management of hereditary angioedema.Submitted by Edileide Reis (leyde-landy@hotmail.com) on 2014-02-19T13:43:29Z No. of bitstreams: 1 Regis A. Campos.pdf: 254414 bytes, checksum: db4489a3c989b1cb781cd78756cb885c (MD5)Approved for entry into archive by Flávia Ferreira (flaviaccf@yahoo.com.br) on 2015-10-13T12:28:26Z (GMT) No. of bitstreams: 1 Regis A. Campos.pdf: 254414 bytes, checksum: db4489a3c989b1cb781cd78756cb885c (MD5)Made available in DSpace on 2015-10-13T12:28:26Z (GMT). No. of bitstreams: 1 Regis A. Campos.pdf: 254414 bytes, checksum: db4489a3c989b1cb781cd78756cb885c (MD5) Previous issue date: 2011http://dx.doi.org/10.1590/S1807-59322011000900021reponame:Repositório Institucional da UFBAinstname:Universidade Federal da Bahia (UFBA)instacron:UFBAHereditary angioedemaC1 inhibitorAsphyxiaAcute surgical abdomenGuidelinesConsensusBrazilian guidelines for the diagnosis and treatment of hereditary angioedemaClinicsinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleBrasilinfo:eu-repo/semantics/openAccessengBianchi, Pedro GiavinaFrança, Alfeu T.Grumach, Anete S.Motta, Abílio A.Fernandes, Fátima R.Campos, Régis de AlbuquerqueValle, Solange O.Rosário, Nelson A.Solé, DirceuBianchi, Pedro GiavinaFrança, Alfeu T.Grumach, Anete S.Motta, Abílio A.Fernandes, Fátima R.Campos, Régis de AlbuquerqueValle, Solange O.Rosário, Nelson A.Solé, DirceuORIGINALRegis A. Campos.pdfRegis A. 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