Gastaut type idiopathic childhood occipital epilepsy

Gastaut type idiopathic childhood occipital epilepsy is an uncommon epileptic syndrome characterised by frequent seizures, most commonly presenting as elementary visual hallucinations or blindness. Other occipital (non-visual) symptoms may also occur. Interictal EEG typically shows occipital paroxys...

Descripción completa

Detalles Bibliográficos
Autores: Ferrari-Marinho, Taissa [UNIFESP], Macedo, Eugenia Fialho [UNIFESP], Neves, Rafael Scarpa da Costa [UNIFESP], Costa, Livia Vianez [UNIFESP], Tudesco, Ivanda de Souza Silva [UNIFESP], Carvalho, Kelly C. [UNIFESP], Carrete, Henrique [UNIFESP], Caboclo, Luis Otávio [UNIFESP], Yacubian, Elza Márcia Targas [UNIFESP], Hamad, Ana Paula [UNIFESP]
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2013
País:Brasil
Institución:Universidade Federal de São Paulo (UNIFESP)
Repositorio:Repositório Institucional da UNIFESP
Idioma:inglés
OAI Identifier:oai:repositorio.unifesp.br:11600/36010
Acceso en línea:http://dx.doi.org/10.1684/epd.2013.0551
http://repositorio.unifesp.br/handle/11600/36010
Access Level:acceso abierto
Palabra clave:idiopathic childhood epilepsy
Gastaut type epilepsy
video-EEG
Descripción
Sumario:Gastaut type idiopathic childhood occipital epilepsy is an uncommon epileptic syndrome characterised by frequent seizures, most commonly presenting as elementary visual hallucinations or blindness. Other occipital (non-visual) symptoms may also occur. Interictal EEG typically shows occipital paroxysms, often with fixation-off sensitivity. Ictal EEG is usually characterised by interruption by paroxysms and sudden appearance of low-voltage, occipital, fast rhythm and/or spikes. Despite well described clinical and EEG patterns, to our knowledge, there are very few reports in the literature with video-EEG recording of either seizure semiology or fixation-off phenomena. We present a video-EEG recording of a 12-year-old girl with Gastaut type epilepsy, illustrating the interictal and ictal aspects of this syndrome. Our aim was to demonstrate the clinical and neurophysiological pattern of a typical seizure of Gastaut type epilepsy, as well as the fixation-off phenomena, in order to further clarify the typical presentation of this syndrome. [Published with video sequences]