Policondrite recidivante na infância: relato de caso e revisão da literatura
Relapsing polychondritis is a rare disease characterized by recurrent episodes of inflammation of the articular, auricular, nasal and laryngotracheal cartilages of variable intensity. Differential diagnosis includes connective tissue diseases, vasculitis and periodic febrile syndromes of childhood....
| Autores: | , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2007 |
| País: | Brasil |
| Institución: | Universidade Federal de São Paulo (UNIFESP) |
| Repositorio: | Repositório Institucional da UNIFESP |
| Idioma: | portugués |
| OAI Identifier: | oai:repositorio.unifesp.br:11600/3716 |
| Acceso en línea: | http://dx.doi.org/10.1590/S0482-50042007000300014 http://repositorio.unifesp.br/handle/11600/3716 |
| Access Level: | acceso abierto |
| Palabra clave: | relapsing polychondritis arthritis inflammation cartilage nose auricular chondritis policondrite recidivante artrite inflamação cartilagem nariz condrite auricular |
| Sumario: | Relapsing polychondritis is a rare disease characterized by recurrent episodes of inflammation of the articular, auricular, nasal and laryngotracheal cartilages of variable intensity. Differential diagnosis includes connective tissue diseases, vasculitis and periodic febrile syndromes of childhood. We report a case of 11 year-old boy with knee arthritis, acute conjunctivitis, ear, nose and upper airway cartilage involvement whose disease was controlled with the use of corticosteroids and immunosuppressive drugs. The clinical and laboratory findings were discussed and compared with case reports from literature. |
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