Dental aspects of Marfan syndrome: case report and review of the literature
The Marfan syndrome is an inheritable connec tive tissue disease, with variable clinical expression. The disease affects specially the skeletal, cardiovascular and ocular systems. Mutations in the gene coding for fi brillin on chromosome 15 (FBN1) are known to cause Marfan syndrome. The dentofacial...
| Autores: | , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2008 |
| País: | Brasil |
| Institución: | Universidade Federal do Rio Grande do Sul (UFRGS) |
| Repositorio: | Revista da Faculdade de Odontologia de Porto Alegre (Online) |
| Idioma: | portugués |
| OAI Identifier: | oai:seer.ufrgs.br:article/6248 |
| Acceso en línea: | https://seer.ufrgs.br/index.php/RevistadaFaculdadeOdontologia/article/view/6248 |
| Access Level: | acceso abierto |
| Palabra clave: | Síndrome de Marfan Odontologia Portadores de necessidades especiais Marfan syndrome Dentistry Disabled persons |
| Sumario: | The Marfan syndrome is an inheritable connec tive tissue disease, with variable clinical expression. The disease affects specially the skeletal, cardiovascular and ocular systems. Mutations in the gene coding for fi brillin on chromosome 15 (FBN1) are known to cause Marfan syndrome. The dentofacial abnormalities present on the disease, as well as other stomatognathic characteristics, make the recognizing and correct managing of these patients important. This paper resumes some of the most important aspects about SM related to Dentistry. |
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