Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome

Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual cas...

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Detalhes bibliográficos
Autores: Tansini, Paula Baldissera, Boff, Ana Letícia, Weber, Magda Blessmann, Bonamigo, Renan Rangel
Formato: artículo
Estado:Versión publicada
Fecha de publicación:2020
País:Brasil
Recursos:Universidade Federal do Rio Grande do Sul (UFRGS)
Repositorio:Repositório Institucional da UFRGS
Idioma:inglés
OAI Identifier:oai:www.lume.ufrgs.br:10183/212341
Acesso em linha:http://hdl.handle.net/10183/212341
Access Level:acceso abierto
Palavra-chave:Pênfigo familiar benigno
Dermatite esfoliativa
Relatos de casos
Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases
Vesiculobullous
Descrição
Resumo:Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.