Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual cas...
| Autores: | , , , |
|---|---|
| Formato: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2020 |
| País: | Brasil |
| Recursos: | Universidade Federal do Rio Grande do Sul (UFRGS) |
| Repositorio: | Repositório Institucional da UFRGS |
| Idioma: | inglés |
| OAI Identifier: | oai:www.lume.ufrgs.br:10183/212341 |
| Acesso em linha: | http://hdl.handle.net/10183/212341 |
| Access Level: | acceso abierto |
| Palavra-chave: | Pênfigo familiar benigno Dermatite esfoliativa Relatos de casos Pemphigus, benign familial Dermatitis, exfoliative Skin diseases Vesiculobullous |
| Resumo: | Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome. |
|---|