Acidóse tubular renal distal manifestando-se com rabdomiólise

Severe hypokalemia is an uncommon cause of rhabdomyolysis. We describe a patient, 28-year-old woman, with distal renal tubular acidosis (DRTA) who developed severe hypokalemia and rhabdomyolysis. Muscle biopsy shows focal muscular necrosis mainly in type II muscle fibers and mild macrophagic reactio...

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Detalles Bibliográficos
Autores: Zanoteli, Edmar [UNIFESP], Oliveira, Acary Souza Bulle [UNIFESP], Tengan, Célia Harumi [UNIFESP], Morita, Maria da Penha Ananias [UNIFESP], Schmidt, Beny [UNIFESP], Gabbai, Alberto Alain [UNIFESP]
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:1994
País:Brasil
Institución:Universidade Federal de São Paulo (UNIFESP)
Repositorio:Repositório Institucional da UNIFESP
Idioma:portugués
OAI Identifier:oai:repositorio.unifesp.br:11600/360
Acceso en línea:http://dx.doi.org/10.1590/S0004-282X1994000400016
http://repositorio.unifesp.br/handle/11600/360
Access Level:acceso abierto
Palabra clave:hypokalemia
rhabdomyolysis
renal tubular acidosis
hipocalemia
rabdomiólise
acidóse tubular renal
Descripción
Sumario:Severe hypokalemia is an uncommon cause of rhabdomyolysis. We describe a patient, 28-year-old woman, with distal renal tubular acidosis (DRTA) who developed severe hypokalemia and rhabdomyolysis. Muscle biopsy shows focal muscular necrosis mainly in type II muscle fibers and mild macrophagic reaction. After correcting the acidosis with oral administration of alkalinizing salts, clinical and laboratory improvement was seen. This clearly establish a causal realtionship between the positive acid balance, hypokalemia and the muscular manifestation in DRTA.